Melnick-Needles Syndrome: Report of a Case Associated with Bilateral Hypoplasia of the Cochlea

Abstract

SUMMARY: Melnick-Needles Syndrome is a rare disorder associated with many abnormalities. This case report describes a patient with Melnick-Needles Syndrome who was found to have bilateral hypoplasia of the cochlea, a finding not previously described in the literature. The case report describes the syndrome and demonstrates the findings on CT and MR imaging of temporal bones.