RT Journal Article
SR Electronic
T1 Lacrimal Location of Sinus Histiocytosis (Destombes-Rosai-Dorfman Disease)
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 498
OP 500
VO 25
IS 3
A1 Azoulay, Robin
A1 Brisse, Hervé
A1 Fréneaux, Paul
A1 Ferey, Solène
A1 Kalifa, Gabriel
A1 Adamsbaum, Catherine
YR 2004
UL http://www.ajnr.org/content/25/3/498.abstract
AB Summary: A 7-year-old West African male patient presented with recurrence of multiple cervical lymphadenopathy. Cervical node biopsy disclosed a sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman-Destombes disease). During follow-up, the patient developed a left orbital mass corresponding to an enlarged lacrimal gland shown by CT. The histologic features of the gland were consistent with the diagnosis, and with steroid treatment, the gland decreased in size. Although rare, the diagnosis of sinus histiocytosis with massive lymphadenopathy has to be considered in cases of lacrimal gland enlargement.