PT  - JOURNAL ARTICLE
AU  - Maki, Daniel D.
AU  - Yousem, David M.
AU  - Corcoran, Celeste
AU  - Galetta, Steven L.
TI  - MR Imaging of Dejerine-Sottas Disease
DP  - 1999 Mar 01
TA  - American Journal of Neuroradiology
PG  - 378--380
VI  - 20
IP  - 3
4099  - http://www.ajnr.org/content/20/3/378.short
4100  - http://www.ajnr.org/content/20/3/378.full
SO  - Am. J. Neuroradiol.1999 Mar 01; 20
AB  - Summary: We report the MR findings in two patients with clinically and histologically proved Dejerine-Sottas disease. One patient had spinal involvement with multiple thickened and clumped nerve roots of the cauda equina; the second had multiple enlarged and enhancing cranial nerves. Although these findings are not specific for Dejerine-Sottas disease, they are suggestive of the diagnosis, which is further corroborated with history and confirmed with sural nerve biopsy and laboratory studies.