RT Journal Article
SR Electronic
T1 Neurocutaneous Melanomatosis with a Rapidly Deteriorating Course
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 287
OP 290
VO 24
IS 2
A1 Chu, Winnie C.W.
A1 Lee, Vincent
A1 Chan, Yu-leung
A1 Shing, Matthew MK
A1 Chik, Ki-wai
A1 Li, Chi-kong
A1 Ma, Kwok-chiu
YR 2003
UL http://www.ajnr.org/content/24/2/287.abstract
AB Summary: Neurocutaneous melanosis is a rare congenital syndrome characterized by large or multiple congenital melanocytic nevi and benign or malignant pigment cell tumors of the leptomeninges. The prognosis is extremely poor for symptomatic patients, even in the absence of malignant melanoma. We present serial MR imaging findings in the brain and spine of a child with congenital giant hairy nevi who developed progressive leptomeningeal melanomatosis and whose neurologic condition rapidly deteriorated.