PT  - JOURNAL ARTICLE
AU  - Takanashi, Jun-ichi
AU  - Barkovich, A. James
AU  - Cheng, Sabrina F.
AU  - Kostiner, Dana
AU  - Baker, John C.
AU  - Packman, Seymour
TI  - Brain MR Imaging in Acute Hyperammonemic Encephalopathy Arising from Late-Onset Ornithine Transcarbamylase Deficiency
DP  - 2003 Mar 01
TA  - American Journal of Neuroradiology
PG  - 390--393
VI  - 24
IP  - 3
4099  - http://www.ajnr.org/content/24/3/390.short
4100  - http://www.ajnr.org/content/24/3/390.full
SO  - Am. J. Neuroradiol.2003 Mar 01; 24
AB  - Summary: The brain MR imaging characteristics of three patients with acute hyperammonemic encephalopathy resulting from late-onset ornithine transcarbomylase deficiency are presented. MR images revealed injury to the cortex, especially the cingulate gyrus and insular cortex, with sparing of the perirolandic and occipital cortices. These findings presumably reflect the distribution of brain injury from hypoperfusion secondary to hyperammonemia. Knowledge of the MR findings may help expedite diagnosis and treatment and prevent chronic impairment.