RT Journal Article
SR Electronic
T1 Susac Syndrome: Report of Four Cases and Review of the Literature
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 382
OP 388
VO 25
IS 3
A1 Do, Tai Hung
A1 Fisch, Christiane
A1 Evoy, François
YR 2004
UL http://www.ajnr.org/content/25/3/382.abstract
AB Summary: Susac syndrome is a rare disease of unknown pathogenesis. It is caused by a microangiopathy affecting the arterioles of the brain, retina, and cochlea, giving the classic clinical triad of subacute encephalopathy, visual loss secondary to retinal branch occlusions, and sensorineural hearing loss. The features of four cases of this syndrome are presented. MR imaging, retinal fluorescein angiography, and audiography findings enable diagnosis. Early therapy may reduce sequelae and improve recovery.