RT Journal Article
SR Electronic
T1 Diffuse CNS Vasculopathy with Chronic Epstein-Barr Virus Infection in X-Linked Lymphoproliferative Disease
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 884
OP 886
VO 27
IS 4
A1 Weeks, J.K.
A1 Helton, K.J.
A1 Conley, M.E.
A1 Onciu, M.
A1 Khan, R.B.
YR 2006
UL http://www.ajnr.org/content/27/4/884.abstract
AB SUMMARY: We report a patient with X-linked lymphoproliferative disease (XLP) who developed multiple central nervous system (CNS) manifestations of Epstein-Barr virus infection. XLP, or Duncan syndrome, is a rare inherited disorder characterized by the inability to clear Epstein-Barr virus infection. In addition to Epstein-Barr virus encephalitis, CNS lymphoproliferative disease, and lymphoma, this patient also developed MR angiographic evidence of diffuse fusiform aneurysmal dilation of intracranial vessels.