Descriptive analysis of patients with DW with brainstem involvement
Variable | |
---|---|
Sex (No.) (%) | |
Male | 29 (39.7%) |
Female | 44 (60.3%) |
Age | |
Age (mo) | 25 mo (IQR = 10 days to 15.6 mo) |
Birth status (No.) (%) | |
Premature | 20 (27.4%) |
Full-term | 35 (47.9%) |
Unknown | 18 (24.7%) |
Imaging features (No.) (%) | |
Severe macrocrania | 24 (32.9%) |
Extreme vermian hypoplasia | 12 (16.4%) |
Cerebellar dysplasia | 27 (37%) |
Anteroposterior disproportion | 67 (91.8%) |
Hydrocephalus | 43 (58.9%) |
Corpus callosum agenesis | 37 (50.7%) |
Interhemispheric cyst | 11 (15.1%) |
Gray matter migration | 18 (24.7%) |
Calcification or hemorrhage | 12 (16.4%) |
Fastigial recess angle (mean) | 167.1° (SD, 46.6°) |
Posterior fossa perimeter (mean) (mm) | 172.4 (SD, 110.6) |
Clinical features (No.) (%) | |
Seizure | 31 (42.5%) |
Artificial airway dependency | 32 (43.8%) |
Enteral feeding tube dependency | 40 (54.8%) |
Mortality | 15 (20.5%) |