Cortical hamartoma perfusion imaging findings in a series of 13 patients evaluated with pulsed arterial spin-labeling
Pt | Age (yr) | Seizures per Week | Seizure Frequency | No. Cortical Hamartomas >1 cm | No. Hyperperfused Hamartomas | No. Hypoperfused Hamartomas | No. Normally Perfused Hamartomas | Mean Normal GM Perfusion (mL/100 g/min) | Mean Hyperperfused Lesions (mL/100 g/min) | Mean Hypoperfused Lesions (mL/100 g/min) |
---|---|---|---|---|---|---|---|---|---|---|
1a | 0.7 | 0 | None | 12 | 0 | 11 | 1 | 63.8 | 26.5 | |
1b | 12 | 0 | 11 | 1 | 67.9 | 26.3 | ||||
2a | 7 | 0 | None | 10 | 0 | 10 | 0 | 116.6 | 63.8 | |
2b | 9 | 0 | 6 | 3 | 123.0 | 79.8 | ||||
3 | 2 | 1 | 1 per week | 21 | 0 | 21 | 0 | 173.6 | 104.6 | |
4a | 8 | 2 | 2 per week, left facial twitch | 9 | 3 | 5 | 1 | 108.1 | 155.1 | 68.1 |
4b | 9 | 3 | 6 | 0 | 112.4 | 154.0 | 35.3 | |||
5 | 7 | 0 | None, last 8 months | 3 | 1 | 2 | 0 | 102.3 | 127.7 | 86.7 |
6 | 23 | 4 | 4 per week, EEG left temporal | 23 | 1 | 21 | 1 | 52.8 | 61.4 | 20.0 |
7 | 5 | 0 | None, last 3 months | 41 | 0 | 41 | 0 | 131.4 | 23.0 | |
8 | 3 | 3 | 3–4 per week | 18 | 1 | 17 | 0 | 163.2 | 186.7 | 61.6 |
9 | 12 | 0 | None last 10 years | 5 | 0 | 5 | 0 | 85.4 | 25.6 | |
10 | 6 | 0 | None last 2 years | 22 | 1 | 21 | 0 | 122.2 | 151.2 | 45.2 |
11 | 3 | 0 | None last 3 months | 19 | 0 | 18 | 1 | 99.6 | 38.9 | |
12 | 10 | 0 | None last 3 months | 8 | 0 | 8 | 0 | 84.6 | 22.8 | |
13 | 11 | 2 | 1–2 per week | 24 | 0 | 24 | 0 | 60.0 | 23.8 |
Note:—Pt indicates patient; EEG, electroencephalogram; GM, gray matter.