Table 1:

Basic clinical data of all subjects with unilateral cochlear nerve deficiency (aplasia and hypoplasia)

CaseAge (yr)SexCochlear Nerve DeficiencyHearing Threshold (PTA) dB HL
RightLeftRightLeft
112MAplasiaNormal10010
210FAplasiaNormal>10020
38FAplasiaNormal>10010
49FAplasiaNormal>11015
514FHypoplasiaNormal1005
68MHypoplasiaNormal>11010
712MNormalAplasia5>110
825FAplasiaNormal10010
99MNormalAplasia10>110
1011MNormalAplasia10>110
1129MNormalAplasia15>110
129FHypoplasiaNormal9010
  • Note:—PTA indicates pure tone average; HL, hearing level.