Comparison between KTS and PWSa

FeatureKTSPWS
Types of vascular malformationsSlow flow; capillary, lymphatic, venousFast flow; capillary, arterial, venous
Color of capillary stainRed to purplishPink and diffuse; multiple capillary stains if RASA1
AV fistulasInsignificantSignificant
Marginal venous anomalyVery commonNot found
Lymphatic vesiclesPresentUncommon
Limb affectedUpper 5%, lower 95%Upper 23%, lower 77%
PrognosisPoor quality of life due to venous insufficiency and complications of lymphatic malformation; risk of pulmonary embolismProgressive symptoms with cutaneous ischemia and possible heart failure
  • a Modified from Reference 5.