Comparison between KTS and PWSa
Feature | KTS | PWS |
---|---|---|
Types of vascular malformations | Slow flow; capillary, lymphatic, venous | Fast flow; capillary, arterial, venous |
Color of capillary stain | Red to purplish | Pink and diffuse; multiple capillary stains if RASA1 |
AV fistulas | Insignificant | Significant |
Marginal venous anomaly | Very common | Not found |
Lymphatic vesicles | Present | Uncommon |
Limb affected | Upper 5%, lower 95% | Upper 23%, lower 77% |
Prognosis | Poor quality of life due to venous insufficiency and complications of lymphatic malformation; risk of pulmonary embolism | Progressive symptoms with cutaneous ischemia and possible heart failure |
a Modified from Reference 5.