Table 1:

Demographic characteristics of patients with primary intracranial sarcoma, DICER1-mutant, included in this case series

Demographic Characteristic (Number Assessed)Finding
Age (8)Mean: 16 years
Standard deviation: 11.57 years
Range: 4–33
Presenting symptoms (7)Headaches: 5
Extremity weakness: 2
Nausea: 2
Numbness: 2
Language deficit: 1
Blurry vision: 1
Unsteady gait: 1
Duration of symptoms (5)Average: 7 days
Range: 1–14 days
DICER1 mutation (8)Yes
Additional mutationsATRX 5/5 patients
TP53 7/7 patients
Other DICER1-related tumors (7)None