Table 1:

Clinical characteristics of patients with amyotrophic lateral sclerosis (ALS)

Patient No./ Age (y)/SexDuration (mo)ALSFRS-RUMN ScoreAffected SideELESC
1/49/M16396LDefinite
2/44/M5253BDefinite
3/68/M52272LProbable
4/54/F6443LDefinite
5/54/M8343BProbable
6/63/M33485LDefinite
7/64/M11403RProbable
8/72/M20425LDefinite
9/58/M10405RDefinite
10/57/M4466RDefinite
11/63/F5474BProbable
12/54/M30405LDefinite
13/39/F50465LPossible
14/56/M13453BPossible
15/49/F4475LProbable
16/69/M60365LDefinite
  • Note:—ALSFRS-R indicates ALS Functional Rating Scale–Revised13; UMN, upper motor neuron; ELESC, El Escorial12; L, left; R, right; B, bilateral.