Table 3:

Intracranial abnormalities in children with ANSDa

Type of Intracranial AbnormalityCochlear Nerve Status
Normal (n = 69)Unilateral CND (n = 19)Bilateral CND (n = 15)
None44 (63.8%)16 (84.2%)6 (40.0%)
Any intracranial abnormality25 (36.2%)3 (15.8%)19 (60.0%)1
    Forebrain malformations3 (4.3%)0 (0.0%)4 (26.7%)
    Mid-/hindbrain malformations7 (10.1%)20 (0.0%)36 (40.0%)2,3
    CSF abnormalities12 (17.4%)3 (11.7%)4 (26.7%)
    Abnormalities of WM16 (23.2%)0 (0.0%)2 (13.3%)
  • a Superscripts denote significant group pair differences: 1, P = .012; 2, P = .010; 3, P = .004.