Article Figures & Data
Figures
- Fig 1.
Case 1. A 51-year-old woman with transthyretine-related FAP.
A, Cervical sagittal T1-weighted image (400/12/2 [TR/TE/NEX]) shows slight hyperintensity of the subpial region, which is observed predominantly at the cervical cord level (arrows).
B, Axial T1-weighted image (500/15/2) at C4 shows slight hyperintensity of the subpial region as well as observed in panel A. Thickening and increase of signal intensity of the dentate ligament (arrow) and the cervical septum (arrowhead) are also observed.
C, Contrast-enhanced T1-weighted image (400/12/2) shows diffuse leptomeningeal enhancement (arrows).
D, Axial 3D-CISS reformation image (12.2/5.9/1) at T9 shows thickening of dura matter (arrows). Thickened dentate ligaments (arrowheads) and cervical septum (long arrow) are also observed.
E, Cervical sagittal 3D-CISS image (12.2/5.9/1) shows longitudinal low signal intensity band parallel to the spinal cord (arrows), which represents thickened dentate ligament.
F, Coronal 3D-CISS image (12.2/5.9/1) shows thickened dura matter (arrowheads), and tortuous veins dorsal to spinal cord are well observed (arrows).
- Fig 2.
Case 2. A 39-year-old man with transthyretine-related FAP.
A, Contrast-enhanced T1-weighted image (400/12/2) shows diffuse leptomeningeal enhancement predominantly in the cervical and upper thoracic region (arrows).
B, Sagittal 3D-CISS image (12.2/5.9/1) shows low-signal-intensity tiny strands dorsal to the spinal cord (arrows), which represent thickened arachnoid tissue. A thickened dentate ligament was also seen on cervical parasagittal 3D-CISS image (not shown).
C, Axial 3D-CISS reformation image (12.2/5.9/1) at C7 shows thickening of dentate ligaments (arrows) and cervical septum (arrowhead). Long arrows indicate ventral and dorsal nerve roots.
D, Axial 3D-CISS reformation image (12.2/5.9/1) at C3 shows thickening of dorsal nerve roots (arrows).
E, Coronal 3D-CISS reformation image (12.2/5.9/1) of dorsal region of lower spinal cord shows low signal intensity tiny strands (arrows), which represent thickened arachnoid tissue.
