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Comparison between KTS and PWSa
Feature KTS PWS Types of vascular malformations Slow flow; capillary, lymphatic, venous Fast flow; capillary, arterial, venous Color of capillary stain Red to purplish Pink and diffuse; multiple capillary stains if RASA1 AV fistulas Insignificant Significant Marginal venous anomaly Very common Not found Lymphatic vesicles Present Uncommon Limb affected Upper 5%, lower 95% Upper 23%, lower 77% Prognosis Poor quality of life due to venous insufficiency and complications of lymphatic malformation; risk of pulmonary embolism Progressive symptoms with cutaneous ischemia and possible heart failure -
a Modified from Reference 5.
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