Volumetric Description of Brain Atrophy in Neuronal Ceroid Lipofuscinosis 2: Supratentorial Gray Matter Shows Uniform Disease Progression

U. Löbel; J. Sedlacik; M. Nickel; S. Lezius; J. Fiehler; I. Nestrasil; A. Kohlschütter; A. Schulz

doi:10.3174/ajnr.A4816

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Volumetric Description of Brain Atrophy in Neuronal Ceroid Lipofuscinosis 2: Supratentorial Gray Matter Shows Uniform Disease Progression

U. Löbel, J. Sedlacik, M. Nickel, S. Lezius, J. Fiehler, I. Nestrasil, A. Kohlschütter and A. Schulz

American Journal of Neuroradiology October 2016, 37 (10) 1938-1943; DOI: https://doi.org/10.3174/ajnr.A4816

U. Löbel

aFrom the Departments of Diagnostic and Interventional Neuroradiology (U.L., J.S., J.F.)

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J. Sedlacik

aFrom the Departments of Diagnostic and Interventional Neuroradiology (U.L., J.S., J.F.)

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M. Nickel

bPediatrics (M.N., A.K., A.S.)

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S. Lezius

cMedical Biometry and Epidemiology (S.L.), University Medical Center Hamburg-Eppendorf, Hamburg, Germany

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J. Fiehler

aFrom the Departments of Diagnostic and Interventional Neuroradiology (U.L., J.S., J.F.)

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I. Nestrasil

dDepartment of Pediatrics (I.N.), University of Minnesota, Minneapolis, Minnesota.

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A. Kohlschütter

bPediatrics (M.N., A.K., A.S.)

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A. Schulz

bPediatrics (M.N., A.K., A.S.)

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vol. 37 no. 10 1938-1943

DOI

https://doi.org/10.3174/ajnr.A4816

PubMed

27231226

Published By

American Journal of Neuroradiology

Print ISSN

0195-6108

Online ISSN

1936-959X

History

Received December 22, 2015
Accepted after revision March 21, 2016
Published online October 7, 2016.

Author Information

U. Löbela,
J. Sedlacika,
M. Nickelb,
S. Leziusc,
J. Fiehlera,
I. Nestrasild,
A. Kohlschütterb and
A. Schulzb

^aFrom the Departments of Diagnostic and Interventional Neuroradiology (U.L., J.S., J.F.)
^bPediatrics (M.N., A.K., A.S.)
^cMedical Biometry and Epidemiology (S.L.), University Medical Center Hamburg-Eppendorf, Hamburg, Germany
^dDepartment of Pediatrics (I.N.), University of Minnesota, Minneapolis, Minnesota.

Please address correspondence to Ulrike Löbel, MD, Department of Diagnostic and Interventional Neuroradiology, O-22, Martinistr 52, 20246 Hamburg, Germany; e-mail: u.loebel{at}uke.de

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U. Löbel, J. Sedlacik, M. Nickel, S. Lezius, J. Fiehler, I. Nestrasil, A. Kohlschütter, A. Schulz

Volumetric Description of Brain Atrophy in Neuronal Ceroid Lipofuscinosis 2: Supratentorial Gray Matter Shows Uniform Disease Progression

American Journal of Neuroradiology Oct 2016, 37 (10) 1938-1943; DOI: 10.3174/ajnr.A4816

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Volumetric Description of Brain Atrophy in Neuronal Ceroid Lipofuscinosis 2: Supratentorial Gray Matter Shows Uniform Disease Progression

U. Löbel, J. Sedlacik, M. Nickel, S. Lezius, J. Fiehler, I. Nestrasil, A. Kohlschütter, A. Schulz

American Journal of Neuroradiology Oct 2016, 37 (10) 1938-1943; DOI: 10.3174/ajnr.A4816

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Enzyme Replacement Therapy for CLN2 Disease: MRI Volumetry Shows Significantly Slower Volume Loss Compared with a Natural History Cohort

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