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Research ArticlePediatric Neuroimaging
Open Access

Characteristic Cochlear Hypoplasia in Patients with Walker-Warburg Syndrome: A Radiologic Study of the Inner Ear in α-Dystroglycan–Related Muscular Disorders

G. Talenti, C. Robson, M.S. Severino, C.A. Alves, D. Chitayat, H. Dahmoush, L. Smith, F. Muntoni, S.I. Blaser and F. D’Arco
American Journal of Neuroradiology January 2021, 42 (1) 167-172; DOI: https://doi.org/10.3174/ajnr.A6858
G. Talenti
aFrom the Department of Diagnostics and Pathology (G.T.), Neuroradiology Unit, Verona University Hospital, Verona, Italy
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C. Robson
bDivision of Neuroradiology (C.R.), Department of Radiology, Boston Children’s Hospital and Harvard Medical School, Boston, Massachusetts
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M.S. Severino
cNeuroradiology Unit (M.S.S.), Istituti di Ricovero e Cura a Carattere Scientifico, Istituto Giannina Gaslini, Genova, Italy
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C.A. Alves
dDepartments of Radiology and Division of Neuroradiology (C.A.A.), Children’s Hospital of Philadelphia, Philadelphia, Pennsylvania
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  • ORCID record for C.A. Alves
D. Chitayat
eThe Prenatal Diagnosis and Medical Genetics Program (D.C.), Department of Obstetrics and Gynecology, Mount Sinai Hospital, University of Toronto, Toronto, Ontario, Canada
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H. Dahmoush
fDepartment of Radiology (H.D.), Lucile Packard Children's Hospital, Stanford University School of Medicine, Stanford, California
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L. Smith
gDental and Maxillofacial Surgery Department (L.S.), Great Ormond Street Hospital, London, UK
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F. Muntoni
hDubowitz Neuromuscular Centre (F.M.), UCL Great Ormond Street Institute of Child Health and Great Ormond Street Hospital, London, UK
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S.I. Blaser
iDivision of Neuroradiology (S.I.B.), Department of Diagnostic Imaging, The Hospital for Sick Children, Toronto, Ontario, Canada
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F. D’Arco
jNeuroradiology Unit (F.D.), Department of Radiology, Great Ormond Street Hospital for Children, National Health Service Trust, London, UK
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G. Talenti, C. Robson, M.S. Severino, C.A. Alves, D. Chitayat, H. Dahmoush, L. Smith, F. Muntoni, S.I. Blaser, F. D’Arco
Characteristic Cochlear Hypoplasia in Patients with Walker-Warburg Syndrome: A Radiologic Study of the Inner Ear in α-Dystroglycan–Related Muscular Disorders
American Journal of Neuroradiology Jan 2021, 42 (1) 167-172; DOI: 10.3174/ajnr.A6858

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Characteristic Cochlear Hypoplasia in Patients with Walker-Warburg Syndrome: A Radiologic Study of the Inner Ear in α-Dystroglycan–Related Muscular Disorders
G. Talenti, C. Robson, M.S. Severino, C.A. Alves, D. Chitayat, H. Dahmoush, L. Smith, F. Muntoni, S.I. Blaser, F. D’Arco
American Journal of Neuroradiology Jan 2021, 42 (1) 167-172; DOI: 10.3174/ajnr.A6858
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