Aggressive Leptomeningeal Hemangioblastomatosis of the Central Nervous System in a Patient with von Hippel-Lindau Disease

A and B, MR axial, postgadolinium images of the suprasellar region, obtained with use of the SPGR technique, demonstrate numerous hemangioblastomatous tumors surrounding the extraorbital parts of the optic nerves, the optic chiasm, the sella, and the arteries of the circle of Willis. C, Sagittal, postcontrast T1-weighted image of the thoracic spine shows diffuse leptomeningeal infiltration by hemangioblastomas.